Q20-Q28Not billable, use a more specific code below
Congenital malformations of the circulatory system (Q20-Q28)
chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities
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Official coding guidelines
From the ICD-10-CM Official Guidelines for Coding and Reporting, FY 2027 (CMS and NCHS). Links open the PDF at the right page.
Assign Q00-QA1 codes for documented congenital anomalies or genetic disorders at any age, coding non-inherent manifestations separately and sequencing Z38 first on the birth admission.
All codes under Q20-Q28
Q20-Q28 can't be used on a claim. Pick a billable code below; grey headings group them.
- Q20Congenital malformations of cardiac chambers and connections
- Q20.0Common arterial trunk
- Q20.1Double outlet right ventricle
- Q20.2Double outlet left ventricle
- Q20.3Discordant ventriculoarterial connection
- Q20.4Double inlet ventricle
- Q20.5Discordant atrioventricular connection
- Q20.6Isomerism of atrial appendages
- Q20.8Other congenital malformations of cardiac chambers and connections
- Q20.9Congenital malformation of cardiac chambers and connections, unspecified
- Q21Congenital malformations of cardiac septa
- Q21.0Ventricular septal defect
- Q21.1Atrial septal defect
- Q21.10Atrial septal defect, unspecified
- Q21.11Secundum atrial septal defect
- Q21.12Patent foramen ovale
- Q21.13Coronary sinus atrial septal defect
- Q21.14Superior sinus venosus atrial septal defect
- Q21.15Inferior sinus venosus atrial septal defect
- Q21.16Sinus venosus atrial septal defect, unspecified
- Q21.19Other specified atrial septal defect
- Q21.2Atrioventricular septal defect
- Q21.20Atrioventricular septal defect, unspecified as to partial or complete
- Q21.21Partial atrioventricular septal defect
- Q21.22Transitional atrioventricular septal defect
- Q21.23Complete atrioventricular septal defect
- Q21.3Tetralogy of Fallot
- Q21.4Aortopulmonary septal defect
- Q21.8Other congenital malformations of cardiac septa
- Q21.9Congenital malformation of cardiac septum, unspecified
- Q22Congenital malformations of pulmonary and tricuspid valves
- Q22.0Pulmonary valve atresia
- Q22.1Congenital pulmonary valve stenosis
- Q22.2Congenital pulmonary valve insufficiency
- Q22.3Other congenital malformations of pulmonary valve
- Q22.4Congenital tricuspid stenosis
- Q22.5Ebstein's anomaly
- Q22.6Hypoplastic right heart syndrome
- Q22.8Other congenital malformations of tricuspid valve
- Q22.9Congenital malformation of tricuspid valve, unspecified
- Q23Congenital malformations of aortic and mitral valves
- Q23.0Congenital stenosis of aortic valve
- Q23.1Congenital insufficiency of aortic valve
- Q23.2Congenital mitral stenosis
- Q23.3Congenital mitral insufficiency
- Q23.4Hypoplastic left heart syndrome
- Q23.8Other congenital malformations of aortic and mitral valves
- Q23.81Bicuspid aortic valve
- Q23.82Congenital mitral valve cleft leaflet
- Q23.88Other congenital malformations of aortic and mitral valves
- Q23.9Congenital malformation of aortic and mitral valves, unspecified
- Q24Other congenital malformations of heart
- Q24.0Dextrocardia
- Q24.1Levocardia
- Q24.2Cor triatriatum
- Q24.3Pulmonary infundibular stenosis
- Q24.4Congenital subaortic stenosis
- Q24.5Malformation of coronary vessels
- Q24.6Congenital heart block
- Q24.8Other specified congenital malformations of heart
- Q24.9Congenital malformation of heart, unspecified
- Q25Congenital malformations of great arteries
- Q25.0Patent ductus arteriosus
- Q25.1Coarctation of aorta
- Q25.2Atresia of aorta
- Q25.21Interruption of aortic arch
- Q25.29Other atresia of aorta
- Q25.3Supravalvular aortic stenosis
- Q25.4Other congenital malformations of aorta
- Q25.40Congenital malformation of aorta unspecified
- Q25.41Absence and aplasia of aorta
- Q25.42Hypoplasia of aorta
- Q25.43Congenital aneurysm of aorta
- Q25.44Congenital dilation of aorta
- Q25.45Double aortic arch
- Q25.46Tortuous aortic arch
- Q25.47Right aortic arch
- Q25.48Anomalous origin of subclavian artery
- Q25.49Other congenital malformations of aorta
- Q25.5Atresia of pulmonary artery
- Q25.6Stenosis of pulmonary artery
- Q25.7Other congenital malformations of pulmonary artery
- Q25.71Coarctation of pulmonary artery
- Q25.72Congenital pulmonary arteriovenous malformation
- Q25.79Other congenital malformations of pulmonary artery
- Q25.8Other congenital malformations of other great arteries
- Q25.9Congenital malformation of great arteries, unspecified
- Q26Congenital malformations of great veins
- Q26.0Congenital stenosis of vena cava
- Q26.1Persistent left superior vena cava
- Q26.2Total anomalous pulmonary venous connection
- Q26.3Partial anomalous pulmonary venous connection
- Q26.4Anomalous pulmonary venous connection, unspecified
- Q26.5Anomalous portal venous connection
- Q26.6Portal vein-hepatic artery fistula
- Q26.8Other congenital malformations of great veins
- Q26.9Congenital malformation of great vein, unspecified
- Q27Other congenital malformations of peripheral vascular system
- Q27.0Congenital absence and hypoplasia of umbilical artery
- Q27.1Congenital renal artery stenosis
- Q27.2Other congenital malformations of renal artery
- Q27.3Arteriovenous malformation (peripheral)
- Q27.30Arteriovenous malformation, site unspecified
- Q27.31Arteriovenous malformation of vessel of upper limb
- Q27.32Arteriovenous malformation of vessel of lower limb
- Q27.33Arteriovenous malformation of digestive system vessel
- Q27.34Arteriovenous malformation of renal vessel
- Q27.39Arteriovenous malformation, other site
- Q27.4Congenital phlebectasia
- Q27.8Other specified congenital malformations of peripheral vascular system
- Q27.9Congenital malformation of peripheral vascular system, unspecified
- Q28Other congenital malformations of circulatory system
- Q28.0Arteriovenous malformation of precerebral vessels
- Q28.1Other malformations of precerebral vessels
- Q28.2Arteriovenous malformation of cerebral vessels
- Q28.3Other malformations of cerebral vessels
- Q28.8Other specified congenital malformations of circulatory system
- Q28.9Congenital malformation of circulatory system, unspecified
Q20-Q28 MS-DRGs
This code does not group to an MS-DRG as a principal diagnosis.
Other codes that refer to Q20-Q28
Notes on these codes point to Q20-Q28.
About the condition
Plain-language background from MedlinePlus (National Library of Medicine), not coding guidance.
Congenital Heart Defects
Congenital heart defects (CHDs) are problems with the structure of the heart. "Congenital" means that that the problems are present at birth. These defects happen when a fetus's heart doesn't develop normally during pregnancy. Congenital heart defects are the most common type of birth defect.
Read more about congenital heart defects on MedlinePlus