G40.83

Non-Billable

ChapterG00–G99

Ranksubcategory

Official Description

Dravet syndrome

Metadata & Insights

•2026 ICD-10-CM Edition - Effective October 1, 2025.
•Non-billable category (requires more specific sub-code).
•Chapter 6: Diseases of the Nervous System (G00-G99).

Instructional Notes

Includes

Polymorphic epilepsy in infancy (PMEI)
Severe myoclonic epilepsy in infancy (SMEI)

General instructions are available for the parent sections:

View CH6 Notes View G40 Notes View G40.8 Notes

Clinical Hierarchy

CH6Diseases of the nervous system (G00-G99)

G40-G47Episodic and paroxysmal disorders (G40-G47)

G40Epilepsy and recurrent seizures

G40.8Other epilepsy and recurrent seizures

G40.83Dravet syndrome

G40.833Dravet syndrome, intractable, with status epilepticus

G40.834Dravet syndrome, intractable, without status epilepticus

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to G40.83:

subcategoryG40.8

Other epilepsy and recurrent seizures

View context instructions

categoryG40

Epilepsy and recurrent seizures

View context instructions

chapterCH6

Diseases of the nervous system (G00-G99)

View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to G40.83. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

7 raw paths

Epilepsy, epileptic, epilepsia (attack) (cerebral) (convulsion) (fit) (seizure)2 unique routes

myoclonus, myoclonic

severe, in infancy (SMEI)→G40.83

polymorphic, in infancy (PMEI)→G40.83

PMEI (polymorphic epilepsy in infancy)1 unique routes

Direct index entry→G40.83

SMEI (severe myoclonic epilepsy in infancy)1 unique routes

Direct index entry→G40.83

Syndrome3 unique routes

Dravet (intractable)→G40.83(3 variants)

with status epilepticus→G40.83

without status epilepticus→G40.83

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

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