All ICD10 Codes

D61.02

Billable
ChapterD50–D89
Ranksubcategory
Official Description

Shwachman-Diamond syndrome

Metadata & Insights
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 3: Diseases of the Blood and Blood-Forming Organs (D50-D89).

Instructional Notes

Code Also
  • , if applicable, associated conditions such as:
  • acute myeloblastic leukemia (C92.0-)
  • exocrine pancreatic insufficiency (K86.81)
  • myelodysplastic syndrome (D46.-)
Use Additional Code
  • code, if applicable, for genetic susceptibility to other malignant neoplasm (Z15.09)
General instructions are available for the parent sections:
View CH3 NotesView D61 Notes

Clinical Hierarchy

BillableHas subcodes
CH3Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
D60-D64Aplastic and other anemias and other bone marrow failure syndromes (D60-D64)
D61Other aplastic anemias and other bone marrow failure syndromes
D61.0Constitutional aplastic anemia
D61.02Shwachman-Diamond syndromeBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to D61.02:

categoryD61
Other aplastic anemias and other bone marrow failure syndromes
View context instructions
chapterCH3
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
View context instructions

Code History

  • FY 2023: This code replaced D61.09 (Other constitutional aplastic anemia)

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 808
Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with MCC
DRG 809
Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with CC
DRG 810
Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders without CC/MCC

Cross Reference

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