I05

Non-Billable
ChapterI00–I99
Rankcategory
Official Description

Rheumatic mitral valve diseases

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Non-billable category (requires more specific sub-code).
  • •Chapter 9: Diseases of the Circulatory System (I00-I99).

CH9 Parent Instructions

Excludes2(Not included here)
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • systemic connective tissue disorders (M30-M36)
  • transient cerebral ischemic attacks and related syndromes (G45.-)

Instructional Notes

Includes
  • conditions classifiable to both I05.0 and I05.2-I05.9, whether specified as rheumatic or not
Excludes1(Not coded here)
  • mitral valve disease specified as nonrheumatic (I34.-)
  • mitral valve disease with aortic and/or tricuspid valve involvement (I08.-)

Clinical Hierarchy

CH9Diseases of the circulatory system (I00-I99)
I05-I09Chronic rheumatic heart diseases (I05-I09)
I05Rheumatic mitral valve diseases
I05.0Rheumatic mitral stenosis
I05.1Rheumatic mitral insufficiency
I05.2Rheumatic mitral stenosis with insufficiency
I05.8Other rheumatic mitral valve diseases
I05.9Rheumatic mitral valve disease, unspecified

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to I05:

chapterCH9
Diseases of the circulatory system (I00-I99)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to I05. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

18 raw paths
Calcification2 unique routes
mitral (valve)(2 variants)
annular
rheumatic→I05
annulus
rheumatic→I05
Deformity1 unique routes
mitral (leaflets) (valve)→I05
Disease, diseased3 unique routes
heart (organic)(2 variants)
mitral→I05(2 variants)
specified NEC→I05
mitral (valve)→I05
Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular)3 unique routes
mitral (chronic) (double) (fibroid) (heart) (inactive) (valve) (with chorea)→I05(3 variants)
specified NEC→I05
with
rheumatic fever (conditions in I00)
inactive or quiescent (with chorea)→I05
Failure, failed1 unique routes
mitral→I05
Fever (inanition) (of unknown origin) (persistent) (with chills) (with rigor)1 unique routes
rheumatic (active) (acute) (chronic) (subacute)
inactive or quiescent with
endocarditis
mitral (valve)→I05
Insufficiency, insufficient3 unique routes
mitral (valve)(3 variants)
rheumatic→I05(2 variants)
with
obstruction or stenosis→I05
with
obstruction or stenosis→I05
Lesion (s) (nontraumatic)1 unique routes
mitral→I05
Sclerosis, sclerotic1 unique routes
mitral→I05
Stenosis, stenotic (cicatricial)2 unique routes
mitral (chronic) (inactive) (valve)→I05(2 variants)
with
incompetency, insufficiency or regurgitation→I05

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

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