I01

Non-Billable
ChapterI00–I99
Rankcategory
Official Description

Rheumatic fever with heart involvement

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Non-billable category (requires more specific sub-code).
  • •Chapter 9: Diseases of the Circulatory System (I00-I99).

CH9 Parent Instructions

Excludes2(Not included here)
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • systemic connective tissue disorders (M30-M36)
  • transient cerebral ischemic attacks and related syndromes (G45.-)

Instructional Notes

Excludes1(Not coded here)
  • chronic diseases of rheumatic origin (I05-I09) unless rheumatic fever is also present or there is evidence of reactivation or activity of the rheumatic process.

Clinical Hierarchy

CH9Diseases of the circulatory system (I00-I99)
I00-I02Acute rheumatic fever (I00-I02)
I01Rheumatic fever with heart involvement
I01.0Acute rheumatic pericarditis
I01.1Acute rheumatic endocarditis
I01.2Acute rheumatic myocarditis
I01.8Other acute rheumatic heart disease
I01.9Acute rheumatic heart disease, unspecified

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to I01:

chapterCH9
Diseases of the circulatory system (I00-I99)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to I01. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

25 raw paths
Arteritis1 unique routes
coronary (artery)
rheumatic→I01
Bouillaud's disease or syndrome (rheumatic heart disease)1 unique routes
Direct index entry→I01
Degeneration, degenerative1 unique routes
myocardial, myocardium (fatty) (hyaline) (senile)
with rheumatic fever (conditions in I00)
active, acute or subacute→I01
Disease, diseased4 unique routes
Bouillaud's (rheumatic heart disease)→I01
heart (organic)(3 variants)
rheumatic (chronic) (inactive) (old) (quiescent) (with chorea)
active or acute→I01
with(2 variants)
rheumatic fever (conditions in I00)(2 variants)
active→I01(2 variants)
specified NEC→I01
Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular)10 unique routes
acute or subacute
rheumatic (aortic) (mitral) (pulmonary) (tricuspid)→I01
aortic (heart) (nonrheumatic) (valve)(3 variants)
rheumatic(2 variants)
active or acute→I01
with mitral disease
active or acute→I01
with
mitral disease
active or acute→I01
mitral (chronic) (double) (fibroid) (heart) (inactive) (valve) (with chorea)(2 variants)
active or acute→I01
with
aortic (valve) disease
active or acute→I01
pulmonary (chronic) (heart) (valve)(2 variants)
acute or subacute
rheumatic→I01
rheumatic (chronic) (inactive) (with chorea)
active or acute→I01
rheumatic (chronic) (inactive) (with chorea)
active or acute (aortic) (mitral) (pulmonary) (tricuspid)→I01
tricuspid (chronic) (heart) (inactive) (rheumatic) (valve) (with chorea)
active or acute→I01
Failure, failed4 unique routes
heart (acute) (senile) (sudden)(2 variants)
congestive(2 variants)
rheumatic (chronic) (inactive) (with chorea)
active or acute→I01
with rheumatic fever (conditions in I00)
active→I01
ventricular(2 variants)
left(2 variants)
rheumatic (chronic) (inactive) (with chorea)
active or acute→I01
with rheumatic fever (conditions in I00)
active→I01
Fever (inanition) (of unknown origin) (persistent) (with chills) (with rigor)1 unique routes
rheumatic (active) (acute) (chronic) (subacute)
active with heart involvement→I01
Hypertrophy, hypertrophic2 unique routes
cardiac (chronic) (idiopathic)(2 variants)
rheumatic (with chorea)
active or acute→I01
with rheumatic fever (conditions in I00)
active→I01
Insufficiency, insufficient1 unique routes
mitral (valve)
rheumatic
active or acute→I01

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

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