I00

Billable
ChapterI00–I99
Rankcategory
Official Description

Rheumatic fever without heart involvement

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 9: Diseases of the Circulatory System (I00-I99).

CH9 Parent Instructions

Excludes2(Not included here)
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • systemic connective tissue disorders (M30-M36)
  • transient cerebral ischemic attacks and related syndromes (G45.-)

Instructional Notes

Includes
  • arthritis, rheumatic, acute or subacute
Excludes1(Not coded here)
  • rheumatic fever with heart involvement (I01.0 -I01.9)

Clinical Hierarchy

CH9Diseases of the circulatory system (I00-I99)
I00-I02Acute rheumatic fever (I00-I02)
I00Rheumatic fever without heart involvement

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to I00:

chapterCH9
Diseases of the circulatory system (I00-I99)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to I00. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

5 raw paths
Erythema, erythematous (infectional) (inflammation)1 unique routes
marginatum
in (due to) acute rheumatic fever→I00
Fever (inanition) (of unknown origin) (persistent) (with chills) (with rigor)1 unique routes
rheumatic (active) (acute) (chronic) (subacute)→I00
Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved)2 unique routes
in (due to)
rheumatic fever→I00
rheumatic→I00
Rheumatic (acute) (subacute)1 unique routes
pneumonia→I00

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 545
Connective Tissue Disorders with MCC
DRG 546
Connective Tissue Disorders with CC
DRG 547
Connective Tissue Disorders without CC/MCC

Cross Reference

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