G71.033

Billable
ChapterG00–G99
Ranksubcategory
Official Description

Limb girdle muscular dystrophy due to dysferlin dysfunction

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 6: Diseases of the Nervous System (G00-G99).

Instructional Notes

Includes
  • Dysferlinopathy
  • LGMD R2 dysferlin-related
  • Limb girdle muscular dystrophy type 2B
  • Miyoshi Myopathy type 1
General instructions are available for the parent sections:
View CH6 NotesView G71 Notes

Clinical Hierarchy

CH6Diseases of the nervous system (G00-G99)
G70-G73Diseases of myoneural junction and muscle (G70-G73)
G71Primary disorders of muscles
G71.0Muscular dystrophy
G71.03Limb girdle muscular dystrophies
G71.033Limb girdle muscular dystrophy due to dysferlin dysfunction

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to G71.033:

categoryG71
Primary disorders of muscles
View context instructions
chapterCH6
Diseases of the nervous system (G00-G99)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to G71.033. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

3 raw paths
Dysferlinopathy1 unique routes
Direct index entry→G71.033
Dystrophy, dystrophia2 unique routes
muscular(2 variants)
limb-girdle(2 variants)
R2 (autosomal recessive)→G71.033
type 2B (autosomal recessive)→G71.033

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 091
Other Disorders of Nervous System with MCC
DRG 092
Other Disorders of Nervous System with CC
DRG 093
Other Disorders of Nervous System without CC/MCC

Cross Reference

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