G40.C09

Billable

ChapterG00–G99

Ranksubcategory

Official Description

Lafora progressive myoclonus epilepsy, not intractable, without status epilepticus

Metadata & Insights

•2026 ICD-10-CM Edition - Effective October 1, 2025.
•Billable/specific code (valid for reimbursement).
•Chapter 6: Diseases of the Nervous System (G00-G99).

Instructional Notes

Includes

Lafora progressive myoclonus epilepsy NOS

General instructions are available for the parent sections:

View CH6 Notes View G40 Notes View G40.C Notes

Clinical Hierarchy

CH6Diseases of the nervous system (G00-G99)

G40-G47Episodic and paroxysmal disorders (G40-G47)

G40Epilepsy and recurrent seizures

G40.CLafora progressive myoclonus epilepsy

G40.C0Lafora progressive myoclonus epilepsy, not intractable

G40.C09Lafora progressive myoclonus epilepsy, not intractable, without status epilepticus

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to G40.C09:

subcategoryG40.C

Lafora progressive myoclonus epilepsy

View context instructions

categoryG40

Epilepsy and recurrent seizures

View context instructions

chapterCH6

Diseases of the nervous system (G00-G99)

View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to G40.C09. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

7 raw paths

Disease, diseased1 unique routes

Lafora body→G40.C09

Epilepsy, epileptic, epilepsia (attack) (cerebral) (convulsion) (fit) (seizure)5 unique routes

Lafora progressive myoclonus→G40.C09

myoclonus, myoclonic(3 variants)

progressive(3 variants)

Lafora→G40.C09(3 variants)

not intractable→G40.C09(2 variants)

without status epilepticus→G40.C09

progressive (familial) myoclonic

Lafora→G40.C09

Lafora disease1 unique routes

Direct index entry→G40.C09

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 023

Craniotomy with Major Device Implant or Acute Complex CNS Principal Diagnosis with MCC or Antineoplastic Implant or Epilepsy with Neurostimulator

Cross Reference

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