E83.82
Non-Billable
ChapterE00–E89
Ranksubcategory
Official Description
Disorders of pyrophosphate metabolism
Metadata & Insights
- •2026 ICD-10-CM Edition - Effective October 1, 2025.
- •Non-billable category (requires more specific sub-code).
- •Chapter 4: Endocrine, Nutritional and Metabolic Diseases (E00-E89).
General instructions are available for the parent sections:
Clinical Hierarchy
CH4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E83Disorders of mineral metabolism
E83.8Other disorders of mineral metabolism
E83.82Disorders of pyrophosphate metabolism
E83.820Generalized arterial calcification of infancy with unspecified genetic causality
E83.821ENPP1 deficiency causing generalized arterial calcification of infancy
E83.822ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2
E83.823ABCC6 deficiency causing generalized arterial calcification of infancy
E83.824ABCC6 deficiency causing pseudoxanthoma elasticum
E83.825CD73 deficiency causing arterial calcification
Applicable Ancestor Context
The following parent sections contain instructions or notes that apply to E83.82:
Alphabetic Index Mentions
These are Diagnosis Index lookup paths that route to E83.82. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.
9 raw paths
Calcification4 unique routes
arterial(4 variants)
Deficiency, deficient5 unique routes
ABCC6(2 variants)
MS-DRG Classification
No direct MS-DRG triggers identified.
Cross Reference
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