Q43.1

Billable

ChapterQ00–Q99

Ranksubcategory

Official Description

Hirschsprung's disease

Metadata & Insights

•2026 ICD-10-CM Edition - Effective October 1, 2025.
•Billable/specific code (valid for reimbursement).
•Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-Q99).

Instructional Notes

Includes

Aganglionosis
Congenital (aganglionic) megacolon

General instructions are available for the parent sections:

View CH17 Notes

Clinical Hierarchy

CH17Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)

Q38-Q45Other congenital malformations of the digestive system (Q38-Q45)

Q43Other congenital malformations of intestine

Q43.1Hirschsprung's disease

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to Q43.1:

chapterCH17

Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)

View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to Q43.1. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

8 raw paths

Aganglionosis (bowel) (colon)1 unique routes

Direct index entry→Q43.1

Dilatation1 unique routes

colon

congenital→Q43.1

Hirschsprung's disease or megacolon1 unique routes

Direct index entry→Q43.1

Ileus (bowel) (colon) (inhibitory) (intestine)1 unique routes

neurogenic

Hirschsprung's disease or megacolon→Q43.1

Macrocolon1 unique routes