Q38.0

Billable

ChapterQ00–Q99

Ranksubcategory

Official Description

Congenital malformations of lips, not elsewhere classified

Metadata & Insights

•2026 ICD-10-CM Edition - Effective October 1, 2025.
•Billable/specific code (valid for reimbursement).
•Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-Q99).

Instructional Notes

Includes

Congenital fistula of lip
Congenital malformation of lip NOS
Van der Woude's syndrome

Excludes1(Not coded here)

cleft lip (Q36.-)
cleft lip with cleft palate (Q37.-)
macrocheilia (Q18.6)
microcheilia (Q18.7)

General instructions are available for the parent sections:

View CH17 Notes View Q38 Notes

Clinical Hierarchy

CH17Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)

Q38-Q45Other congenital malformations of the digestive system (Q38-Q45)

Q38Other congenital malformations of tongue, mouth and pharynx

Q38.0Congenital malformations of lips, not elsewhere classified

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to Q38.0:

categoryQ38

Other congenital malformations of tongue, mouth and pharynx

View context instructions

chapterCH17

Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)

View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to Q38.0. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

7 raw paths

Agenesis1 unique routes

lip→Q38.0

Anomaly, anomalous (congenital) (unspecified type)1 unique routes

lip→Q38.0

Deformity1 unique routes

lip (acquired) NEC

congenital→Q38.0

Ectropion1 unique routes

lip (acquired)

congenital→Q38.0

Fistula (cutaneous)1 unique routes