Q02

Billable
ChapterQ00–Q99
Rankcategory
Official Description

Microcephaly

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-Q99).

CH17 Parent Instructions

Excludes2(Not included here)
  • inborn errors of metabolism (E70-E88)

Instructional Notes

Includes
  • hydromicrocephaly
  • micrencephalon
Excludes1(Not coded here)
  • Meckel-Gruber syndrome (Q61.9)
Code First
  • , if applicable, congenital Zika virus disease

Clinical Hierarchy

CH17Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
Q00-Q07Congenital malformations of the nervous system (Q00-Q07)
Q02Microcephaly

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to Q02:

chapterCH17
Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to Q02. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

19 raw paths
Absence (of) (organ or part) (complete or partial)1 unique routes
skull bone (congenital)
with
microcephaly→Q02
Agenesis1 unique routes
skull (bone)
with
microcephaly→Q02
Anomaly, anomalous (congenital) (unspecified type)2 unique routes
bone
skull
with
microcephaly→Q02
skull
with
microcephaly→Q02
Deformity1 unique routes
skull (acquired)
congenital
with
microcephaly→Q02
Distortion (s) (congenital)1 unique routes
skull bone (s) NEC
with
microcephaly→Q02
Hydromicrocephaly1 unique routes
Direct index entry→Q02
Hypoplasia, hypoplastic3 unique routes
brain→Q02
cephalic→Q02
skull (bone)
with
microcephaly→Q02
Idiot, idiocy (congenital)1 unique routes
microcephalic→Q02
Imperfect1 unique routes
closure (congenital)
skull
with
microcephaly→Q02
Micrencephalon, micrencephaly1 unique routes
Direct index entry→Q02
Microcephalus, microcephalic, microcephaly1 unique routes
Direct index entry→Q02
Microencephalon1 unique routes
Direct index entry→Q02
Nondevelopment1 unique routes
brain→Q02
Oligoencephalon1 unique routes
Direct index entry→Q02
Undeveloped, undevelopment2 unique routes
brain (congenital)→Q02
cerebral (congenital)→Q02

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 091
Other Disorders of Nervous System with MCC
DRG 092
Other Disorders of Nervous System with CC
DRG 093
Other Disorders of Nervous System without CC/MCC
DRG 791
Prematurity with Major Problems
DRG 793
Full Term Neonate with Major Problems

Cross Reference

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