Q00.1

Billable
ChapterQ00–Q99
Ranksubcategory
Official Description

Craniorachischisis

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-Q99).
General instructions are available for the parent sections:
View CH17 Notes

Clinical Hierarchy

CH17Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
Q00-Q07Congenital malformations of the nervous system (Q00-Q07)
Q00Anencephaly and similar malformations
Q00.1Craniorachischisis

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to Q00.1:

chapterCH17
Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to Q00.1. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

1 raw paths
Craniorachischisis (totalis)1 unique routes
Direct index entry→Q00.1

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 091
Other Disorders of Nervous System with MCC
DRG 092
Other Disorders of Nervous System with CC
DRG 093
Other Disorders of Nervous System without CC/MCC
DRG 791
Prematurity with Major Problems
DRG 793
Full Term Neonate with Major Problems

Cross Reference

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