J84.1

Non-Billable
ChapterJ00–J99
Ranksubcategory
Official Description

Other interstitial pulmonary diseases with fibrosis

Metadata & Insights
  • •2026 ICD-10-CM Edition - Effective October 1, 2025.
  • •Non-billable category (requires more specific sub-code).
  • •Chapter 10: Diseases of the Respiratory System (J00-J99).

Instructional Notes

Excludes1(Not coded here)
  • pulmonary fibrosis (chronic) following radiation (J70.1)
Code Also
  • , if applicable, pulmonary fibrosis (chronic) due to inhalation of chemicals, gases, fumes or vapors (J68.4)
General instructions are available for the parent sections:
View CH10 NotesView J84 Notes

Clinical Hierarchy

CH10Diseases of the respiratory system (J00-J99)
J80-J84Other respiratory diseases principally affecting the interstitium (J80-J84)
J84Other interstitial pulmonary diseases
J84.1Other interstitial pulmonary diseases with fibrosis
J84.10Pulmonary fibrosis, unspecified
J84.11Idiopathic interstitial pneumonia
J84.17Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to J84.1:

categoryJ84
Other interstitial pulmonary diseases
View context instructions
chapterCH10
Diseases of the respiratory system (J00-J99)
View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to J84.1. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

25 raw paths
Alveolitis1 unique routes
fibrosing (cryptogenic) (idiopathic)→J84.1
Block, blocked1 unique routes
alveolocapillary→J84.1
Bronchiolitis (acute) (infective) (subacute)1 unique routes
respiratory, interstitial lung disease→J84.1
Cirrhosis, cirrhotic (hepatic) (liver)2 unique routes
lung (chronic)→J84.1
pulmonary→J84.1
Disease, diseased2 unique routes
lung(2 variants)
interstitial(2 variants)
respiratory bronchiolitis→J84.1
with progressive fibrotic phenotype, in diseases classified elsewhere→J84.1
Fibrosis, fibrotic10 unique routes
lung (atrophic) (chronic) (confluent) (massive) (perialveolar) (peribronchial)→J84.1(8 variants)
capillary→J84.1
diffuse (idiopathic)→J84.1(4 variants)
chemicals, gases, fumes or vapors (inhalation)→J84.1
interstitial→J84.1(2 variants)
acute→J84.1
idiopathic→J84.1
postinflammatory→J84.1
pulmonary→J84.1(2 variants)
idiopathic→J84.1
Hamman-Rich syndrome1 unique routes
Direct index entry→J84.1
Induration, indurated1 unique routes
lung (black) (chronic) (fibroid)→J84.1
Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved)6 unique routes
cryptogenic organizing→J84.1
desquamative interstitial→J84.1
interstitial(4 variants)
chronic→J84.1
desquamative→J84.1
due to(2 variants)
collagen vascular disease→J84.1
known underlying cause→J84.1

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

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