All ICD10 Codes

Q33.0

Billable
ChapterQ00–Q99
Ranksubcategory
Official Description

Congenital cystic lung

Metadata & Insights
  • •Billable/specific code (valid for reimbursement).
  • •Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-Q99).

Instructional Notes

Includes
  • Congenital cystic lung disease
  • Congenital honeycomb lung
  • Congenital polycystic lung disease
Excludes1(Not coded here. Use a different code.)
  • cystic fibrosis (E84.0)
  • cystic lung disease, acquired or unspecified (J98.4)
General instructions are available for the parent sections:
View CH17 Notes

Clinical Hierarchy

BillableHas subcodes
CH17Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
Q30-Q34Congenital malformations of the respiratory system (Q30-Q34)
Q33Congenital malformations of lung
Q33.0Congenital cystic lungBillable

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to Q33.0:

chapterCH17
Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
View context instructions

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 205
Other Respiratory System Diagnoses with MCC
DRG 206
Other Respiratory System Diagnoses without MCC

Cross Reference

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