H49.81

Non-Billable

ChapterH00–H59

Ranksubcategory

Official Description

Kearns-Sayre syndrome

Metadata & Insights

•2026 ICD-10-CM Edition - Effective October 1, 2025.
•Non-billable category (requires more specific sub-code).
•Chapter 7: Diseases of the Eye and Adnexa (H00-H59).

Instructional Notes

Includes

Progressive external ophthalmoplegia with pigmentary retinopathy

Code Also

, if applicable, other manifestations, such as:
heart block (I45.9)

General instructions are available for the parent sections:

View CH7 Notes View H49-H52 Notes View H49 Notes

Clinical Hierarchy

CH7Diseases of the eye and adnexa (H00-H59)

H49-H52Disorders of ocular muscles, binocular movement, accommodation and refraction (H49-H52)

H49Paralytic strabismus

H49.8Other paralytic strabismus

H49.81Kearns-Sayre syndrome

H49.811Kearns-Sayre syndrome, right eye

H49.812Kearns-Sayre syndrome, left eye

H49.813Kearns-Sayre syndrome, bilateral

H49.819Kearns-Sayre syndrome, unspecified eye

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to H49.81:

categoryH49

Paralytic strabismus

View context instructions

blockH49-H52

Disorders of ocular muscles, binocular movement, accommodation and refraction (H49-H52)

View context instructions

chapterCH7

Diseases of the eye and adnexa (H00-H59)

View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to H49.81. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

3 raw paths

Kearns-Sayre syndrome1 unique routes

Direct index entry→H49.81

Strabismus (congenital) (nonparalytic)2 unique routes

paralytic(2 variants)

Kearns-Sayre syndrome→H49.81

ophthalmoplegia (external)

progressive

with pigmentary retinopathy→H49.81

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

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