G71.036

Billable

ChapterG00–G99

Ranksubcategory

Official Description

Limb girdle muscular dystrophy due to fukutin related protein dysfunction

Metadata & Insights

•2026 ICD-10-CM Edition - Effective October 1, 2025.
•Billable/specific code (valid for reimbursement).
•Chapter 6: Diseases of the Nervous System (G00-G99).

Instructional Notes

Includes

LGMD R9 FKRP-related
Limb girdle muscular dystrophy due to FKRP deficiency
Limb girdle muscular dystrophy type 2I

General instructions are available for the parent sections:

View CH6 Notes View G71 Notes

Clinical Hierarchy

CH6Diseases of the nervous system (G00-G99)

G70-G73Diseases of myoneural junction and muscle (G70-G73)

G71Primary disorders of muscles

G71.0Muscular dystrophy

G71.03Limb girdle muscular dystrophies

G71.036Limb girdle muscular dystrophy due to fukutin related protein dysfunction

Applicable Ancestor Context

The following parent sections contain instructions or notes that apply to G71.036:

categoryG71

Primary disorders of muscles

View context instructions

chapterCH6

Diseases of the nervous system (G00-G99)

View context instructions

Alphabetic Index Mentions

These are Diagnosis Index lookup paths that route to G71.036. Use them as entry terms for search, then confirm final coding instructions in the Tabular List and notes above.

3 raw paths

Dystrophy, dystrophia3 unique routes

muscular(3 variants)

limb-girdle(3 variants)

due to

R9 (autosomal recessive)→G71.036

type 2I (autosomal recessive)→G71.036

MS-DRG Classification

2026 v43.1

This code is grouped within the following Diagnosis Related Group(s) for clinical reimbursement:

DRG 091

Other Disorders of Nervous System with MCC

DRG 092

Other Disorders of Nervous System with CC

DRG 093

Other Disorders of Nervous System without CC/MCC

Cross Reference

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