C00

Non-Billable
ChapterC00–D49
Rankcategory
Official Description

Malignant neoplasm of lip

Metadata & Insights
  • 2026 ICD-10-CM Edition - Effective October 1, 2025.
  • Non-billable category (requires more specific sub-code).
  • Chapter 2: Neoplasms (C00-D49).

Instructional Notes

Excludes1(Not coded here)
  • malignant melanoma of lip (C43.0)
  • Merkel cell carcinoma of lip (C4A.0)
  • other and unspecified malignant neoplasm of skin of lip (C44.0-)
Use Additional Code
  • code to identify:
  • alcohol abuse and dependence (F10.-)
  • history of tobacco dependence (Z87.891)
  • tobacco dependence (F17.-)
  • tobacco use (Z72.0)

Clinical Hierarchy

CH2Neoplasms (C00-D49)
C00-C14Malignant neoplasms of lip, oral cavity and pharynx (C00-C14)
C00Malignant neoplasm of lip
C00.0Malignant neoplasm of external upper lip
C00.1Malignant neoplasm of external lower lip
C00.2Malignant neoplasm of external lip, unspecified
C00.3Malignant neoplasm of upper lip, inner aspect
C00.4Malignant neoplasm of lower lip, inner aspect
C00.5Malignant neoplasm of lip, unspecified, inner aspect
C00.6Malignant neoplasm of commissure of lip, unspecified
C00.8Malignant neoplasm of overlapping sites of lip
C00.9Malignant neoplasm of lip, unspecified

MS-DRG Classification

2026

No direct MS-DRG triggers identified.

Cross Reference

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